Symptomatic intrasellar hemangioblastoma in a child treated with subtotal resection and adjuvant radiosurgery: Case report

Paul D. Sawin, Kenneth A. Follett, B. Chen Wen, Edward R. Laws

Research output: Contribution to journalArticle

29 Citations (Scopus)

Abstract

The first documented case of a symptomatic intrasellar hemangioblastoma is described, occurring in an 11-year-old girl with stigmata of von Hippel-Lindau disease who presented with headaches, progressive bitemporal hemianopsia, and adenohypophysial dysfunction. A subtotal resection of the lesion was achieved with two separate surgical procedures: a transsphenoidal approach and a subfrontal craniotomy. Subsequent growth of residual tumor was treated with combined conventional radiotherapy and stereotactic radiosurgery. Two years following completion of these adjuvant therapies, no residual tumor was evident on magnetic resonance imaging. Previous experience with hemangioblastoma in this region, as well as the rationale for radiotherapy in the treatment of incompletely resected lesions, is reviewed.

Original languageEnglish (US)
Pages (from-to)1046-1050
Number of pages5
JournalJournal of neurosurgery
Volume84
Issue number6
DOIs
StatePublished - Jun 1996

Fingerprint

Hemangioblastoma
Radiosurgery
Residual Neoplasm
Radiotherapy
von Hippel-Lindau Disease
Hemianopsia
Christianity
Craniotomy
Headache
Magnetic Resonance Imaging
Therapeutics
Growth

Keywords

  • Children
  • Hemangioblastoma
  • Pituitary
  • Radiation therapy
  • Radiosurgery
  • Von Hippel-Lindau disease

ASJC Scopus subject areas

  • Surgery
  • Clinical Neurology

Cite this

Symptomatic intrasellar hemangioblastoma in a child treated with subtotal resection and adjuvant radiosurgery : Case report. / Sawin, Paul D.; Follett, Kenneth A.; Wen, B. Chen; Laws, Edward R.

In: Journal of neurosurgery, Vol. 84, No. 6, 06.1996, p. 1046-1050.

Research output: Contribution to journalArticle

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