Neuro-Ophthalmic Presentation of Neuro-Sweet Disease

Padmaja Sudhakar, Stuart Tobin, William O Connor, Sachin Kedar

Research output: Contribution to journalArticle

1 Scopus citations

Abstract

Acute febrile neutrophilic dermatosis (Sweet syndrome) is a systemic inflammatory condition usually associated with autoimmune or neoplastic processes and characterised by inflammatory dermatologic lesions such as erythematous plaques and papules associated with fever and leukocytosis. Neurological and ophthalmological involvement is rare. The authors describe an unusual case of Sweet syndrome associated with microscopic polyangiitis presenting with papilloedema, anterior uveitis, and skin rash. Years later, he developed acute posterior multifocal placoid pigment epitheliopathy. Treatment with immunosuppressive medications led to a relapsing remitting course with maximum benefit from use of steroids. The authors describe the difficulties in diagnosis and treatment of this rare case.

Original languageEnglish (US)
Pages (from-to)202-206
Number of pages5
JournalNeuro-Ophthalmology
Volume41
Issue number4
DOIs
StatePublished - Jul 4 2017

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Keywords

  • APMPPE
  • Sweet syndrome
  • microscopic polyangiitis
  • neuro-Sweet
  • papilloedema

ASJC Scopus subject areas

  • Ophthalmology
  • Clinical Neurology

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