Definition of inseparably fused ventricular myocardium in thoracopagus

Fetal echocardiographic utility and pathologic refinement

David Alan Danford, Bruce M. McManus, Stephen M. Nielsen, Michael G. Levine, Howard William Needelman

Research output: Contribution to journalArticle

9 Citations (Scopus)

Abstract

Correlative echocardiographic and pathological findings in a thoracopagus with conjoined hearts are reported. One twin had tricuspid atresia with discordant atrioventricular connections and concordant ventriculoarterial connections. The morphologic right ventricle was hypoplastic and there was a large muscular ventricular septal defect. The other twin had hypoplasia of the mitral valve anulus and left ventricle with double-outlet right ventricle and pulmonary valve atresia. The tricuspid valve was severely insufficient in part because of a large orifice and redundant, elongated leaflets with abnormal chordal attachments. The left ventricles of these two twins shared a perforated common "free wall" with at least two large defects allowing mixing of the circulations at that level. Not all anatomic details were established conclusively by fetal echocardiography; however, sufficient diagnostic information was obtained to support a decision not to aggressively resuscitate these twins after elective cesarean delivery at 31 weeks' gestation.

Original languageEnglish (US)
Pages (from-to)242-246
Number of pages5
JournalPediatric Cardiology
Volume14
Issue number4
DOIs
StatePublished - Oct 1 1993

Fingerprint

Heart Ventricles
Myocardium
Tricuspid Atresia
Double Outlet Right Ventricle
Pulmonary Atresia
Tricuspid Valve
Ventricular Heart Septal Defects
Mitral Valve
Echocardiography
Pregnancy

Keywords

  • Congenital heart disease
  • Fetal echocardiography
  • Thoracopagus

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Cardiology and Cardiovascular Medicine

Cite this

Definition of inseparably fused ventricular myocardium in thoracopagus : Fetal echocardiographic utility and pathologic refinement. / Danford, David Alan; McManus, Bruce M.; Nielsen, Stephen M.; Levine, Michael G.; Needelman, Howard William.

In: Pediatric Cardiology, Vol. 14, No. 4, 01.10.1993, p. 242-246.

Research output: Contribution to journalArticle

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