Adult onset buphthalmos in a patient with marfan syndrome

Aaron M. Alme, David D. Ingvoldstad, Thomas W. Hejkal, Eyal Margalit

Research output: Contribution to journalArticle

2 Citations (Scopus)

Abstract

PURPOSE: To report a Marfan patient with an adult onset of buphthalmos. DESIGN: Observational case report. METHODS: Review of clinical, photographic, and ultrasound data of a 20-year-old Marfan patient who underwent an intraocular lens implantation complicated by late retinal detachment, chronic hyphema, and elevated intraocular pressure (IOP). RESULTS: A 6-month period of IOP between 25 and 30 mm Hg resulted in a 3.75 mm increase in axial length, a 1-mm increase in corneal diameter, and a 2 mm increase in exophthalmos. CONCLUSIONS: Buphthalmos secondary to long-term ocular hypertension can occur in an adult patient with Marfan syndrome presumably because of abnormal collagen structure. Thus, Marfan patients with high IOP should be treated aggressively to avoid optic nerve damage and other anatomic and structural changes.

Original languageEnglish (US)
Pages (from-to)567-568
Number of pages2
JournalJournal of Glaucoma
Volume17
Issue number7
DOIs
StatePublished - Oct 1 2008

Fingerprint

Hydrophthalmos
Marfan Syndrome
Intraocular Pressure
Hyphema
Ocular Hypertension
Intraocular Lens Implantation
Exophthalmos
Retinal Detachment
Optic Nerve
Collagen

Keywords

  • Buphthalmos
  • Exophthalmos
  • Marfan syndrome
  • Scleral buckle

ASJC Scopus subject areas

  • Ophthalmology

Cite this

Alme, A. M., Ingvoldstad, D. D., Hejkal, T. W., & Margalit, E. (2008). Adult onset buphthalmos in a patient with marfan syndrome. Journal of Glaucoma, 17(7), 567-568. https://doi.org/10.1097/IJG.0b013e3181622550

Adult onset buphthalmos in a patient with marfan syndrome. / Alme, Aaron M.; Ingvoldstad, David D.; Hejkal, Thomas W.; Margalit, Eyal.

In: Journal of Glaucoma, Vol. 17, No. 7, 01.10.2008, p. 567-568.

Research output: Contribution to journalArticle

Alme, AM, Ingvoldstad, DD, Hejkal, TW & Margalit, E 2008, 'Adult onset buphthalmos in a patient with marfan syndrome', Journal of Glaucoma, vol. 17, no. 7, pp. 567-568. https://doi.org/10.1097/IJG.0b013e3181622550
Alme, Aaron M. ; Ingvoldstad, David D. ; Hejkal, Thomas W. ; Margalit, Eyal. / Adult onset buphthalmos in a patient with marfan syndrome. In: Journal of Glaucoma. 2008 ; Vol. 17, No. 7. pp. 567-568.
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